顳骨之纖維性發育不良症－病例報告

Fibrous Dysplasia of the Temporal Bone - Case Report

李明儒(Ming-Ju Lee) ； 李慈芸(Tsu-Yun Lee)

《中華民國耳鼻喉科醫學會雜誌》 32卷1期 (1997/02) Pp. 74-78

https://doi.org/10.6286/1997.32.1.74

摘要

纖維性發育不良症是一種良性的疾病，主要的變化是正常的骨被結締組織、纖維母細胞及類骨組織所取代，因其不正常的增生，造成壓迫形成薄如蛋殼般的骨皮質部。多發生於長骨、助骨及頭顱顏面骨。本科於1995年2月經歷1例8歲男童，以耳後膨出及耳塞感為表徵，高解像電腦斷層顯示病灶位於顳骨之乳突部，經手術部分切除，病理診斷為顳骨之纖維性發育不良症，手術後15個月，狀況穩定。

關鍵字

單骨性 ； 多骨性 ； 纖維性發育不良症

並列摘要

Fibrous dysplasia is a benign disorder. A hallmark of fibrous dysplasia is that normal bone is replaced by abnormal proliferation of connective tissue, fibroblast and osseous tissues in the medullary cavity that eventually erodes the cortex into a thin shell. It can affect long bones, ribs and craniofacial bones. We experienced a case of eight year-old boy who presented with postauricular swelling and ear fullness in February, 1995. High-resolution comput-erized tomography revealed the mastoid of the temporal bone was involved. Partial excision of mastoid lesion was performed and the pathology report disclosed fibrous dysplasia. The postoperative course was stable and no swelling of postauricular area was noted after fifeen months’ follow up.

並列關鍵字

monostotic ； polyostotic ； fibrous dysplasia