第一鰓裂異常－病例報告

First Branchial Cleft Anomaly - Case Report

莊永勳(Yung-Hsun Chuang) ； 張正權(Cheng-Chuan Chang)

《中華民國耳鼻喉科醫學會雜誌》 32卷5期 (1997/10) Pp. 468-472

https://doi.org/10.6286/1997.32.5.468

摘要

一般而言，先夾鰓裂異常以第二鰓裂異常的發生率最高，而第一鰓裂異常是一很罕見的疾病，約佔所有鰓裂異常的1~8%。Work於西元1972年將第一鰓裂異常分為兩型，第一型源自外胚層，為膜性外耳道的複製物，第二型源自外胚層及中胚層，為膜性外耳道與耳廓的複製物。
本科於民國83年4月間，經歷一23歲男性病例，主訴自幼常發生右耳耳漏及耳下腫塊，曾至其它醫院估過次切開引流手術，仍一復發，理學檢查發現耳後下及耳道下壁各有一開口。患者經住院接受腮腺淺葉切除，面神經何留手侑廔管切除，術後情況良，至今未曾復發。(中耳醫誌 1997;32:468-472)

關鍵字

第一鰓裂異常 ； 廔管 ； 囊腫

並列摘要

First branchial cleft anomaly is a rare diease. It takes place in 1~8%of all congenital branchial cleft anomalies. In 1972, Work has classified first branchial cleft anomaly into two types. Type I is purely ectodermal and it is the duplication of the membranous external audiotory canal. Type II exhibits ectodermal and mesodermal elements and is the duplication of the membranous external auditory canal and pinna.
On April 1994, we experienced a case of first branchial cleft anomaly. The patient complained of an infra-auricular mass and right otorrhea off and on since childhood. He had received the procedure of incision and drainage several times at toher hospitals. Physical examination revelaed a pustulous fistula between the right infra-auricular region and the inferior wall of the external auditory canal. Fistulectomy combined with superficial parotid lobectomy and facial nerve dissection was done. There has been no recurrence till now.

並列關鍵字

first branchial cleft anomaly ； fistula ； cyst