Acute segmental obstructing enteritis (ASOE) is an uncommon inflammatory disorder of childhood that usually mimics mechanical upper intestinal obstruction or an acute abdomen. A number of children with ASDE associated with or without Henoch-Schonlein purpura (HSP) have been observed at our department. The most common complaint is intermittent severe cramping abdominal pain with signs of intestinal obstruction that may be severe and associated with vomiting. Stools may show gross or occult blood and bilious vomiting or hematemesis may also be present. Early diagnosis can prevent unnecessary surgical intervention and reduce morbidity.