Orbital Hemangiopericytoma - A Case Report

眼眶內血管週皮細胞瘤 ─ 病例報告

李永誠(Yang-Chen Lee) ； 王志生(Jyh-Seng Wang) ； 徐正雄(Jeng-Shyong Shyu)

《The Kaohsiung Journal of Medical Sciences》 19卷1期 (2003/01) Pp. 33-37

https://doi.org/10.6452/KJMS.200301.0033

摘要

本病例報告一位50歲男性患者，主訴右眼球凸出長達10年，並且在最近半年來，右眼視力下降至僅辦手動視力，經眼眶電腦斷層發現右眼球後有一巨大腫瘤，且合併視神經壓迫。患者隨後接受眼眶外側切開術切除腫瘤。經病理報告顯示為眼眶內血管週皮細胞瘤。該患者在一個月後接受右眼成熟形白內障囊內移除合併人工水晶體置入術，外觀及視力方面皆獲得極大的改善。在隨後兩年的追蹤檢查下(包括胸腹部電腦斷層)並未發現腫瘤復發情形。眼眶內血管週皮細胞瘤是屬於潛在惡性腫瘤，經由完整的切除術僅可以降低復發率且可以獲得良好的癒後。

關鍵字

眼眶內血管週皮細胞瘤 ； 右眼球凸 ； 眼眶外側切開術

並列摘要

Abstract: A 50-year-old male presented with progressive proptosis in the right eye for 10 years. Decreased visual acuity to hand-motion level was also noted. Orbital computed tomography revealed a large homogenously enhanced mass lesion in the right retrobulbar region with optic nerve compression. The remainder of the ocular examination was normal, except for right mature cataract. The tumor was completely removed through lateral orbitotomy. Histologic findings showed a picture of hemangiopericytoma. One month after cataract extraction and intraocular lens implantation in the right eye, the patient had restored vision. Through 2 years' follow-up, no more orbital tumor was noted. Orbital hemangiopericytoma may have potentially malignant behavior, and a high local recurrence rate if incompletely excised. Complete, intact removal prevents tumor recurrence and provides a good result.

並列關鍵字

hemangiopericytoma ； proptosis ； orbitotomy