眼窩惡性橫紋肌肉瘤是兒童中最常見的原發性眼窩惡性腫瘤,成人則較為罕見。其病理型多屬於胚胎型或肺泡型。臨床表現以眼球突出為主。本篇報告兩個表現較為特殊的惡性橫紋肌肉瘤的病例。病例一為33歲的成年人,病理型為胚胎型,臨床上並未出現眼球突出,而是以動眼神經麻痺及視神經病變來表現。病例二為17歲的青少年,病理型與一般不同,為多形型,臨床上則以眼球突出和眼球移位來表現。兩者均接受了手術切除、化學治療及放射線治療,現情況良好,無復發跡象。此症經過適當的合併治療後,患者的存活率可達百分之九十,所以正確的診斷是相當重要的。
Orbital rhabdomyosarcoma, the most common primary orbital malignant tumor in children, is only occasionally seen in adults. The tumor is classified into four subtypes: embryonal, botryoid, alveolar, and pleomorphic. Two cases of orbital rhabdomyosarcoma were reported here. Case 1, a 33-year-old female, developed optic neuropathy and oculomotor palsy in left eye. Image study revealed a tumor shadow within muscle cone, inferior to the optic nerve. The tumor was excised and the pathological report was embryonal rhabdomyosarcoma. Case 2, a 17-year-old female, suffered from exophthalmos and globe displacement in right eye. Orbital exenteration was performed and the pathological report was pleomorphic rhabdomyosarcoma.