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  • 期刊

Primary Synovial Sarcoma of the Mediastinum: A Case Report

原發性縱膈腔滑膜肉瘤-病例報告

摘要


滑膜肉瘤是一種影響四肢軟組織的惡性腫瘤,通常發生在青少年或年紀輕的成人。原發性縱膈腔滑膜肉瘤甚為罕見且最近才被報告。我們報告一個一開始是以背痛來表現的病例。胸部X光片和電腦斷層均顯示右側巨大腫瘤併肋膜積液。電腦斷層導引切片診斷為原發性縱膈腔滑膜肉瘤,全身性檢查顯示無遠端轉移跡象。病人接受姑息性切除性手術,但對於術後之放射線治療和化學藥物治療反應不佳。病人於術後六個月死亡。原發性縱膈腔滑膜肉瘤相當罕見,目前並無標準的治療方法。廣泛性的切除是最重要的治療方式。我們報告此一罕見疾病並回顧相關文獻。

並列摘要


Synovial sarcoma is a malignant neoplasm predominantly affecting the soft tissues of the extremities of adolescents and young adults. Primary mediastinal synovial sarcomas are rare and have been recognized only recently. We report a case of this rare disease with the initial presentation of back pain. Chest plain film and computerized tomography revealed a huge right-side tumor mass with pleural effusion. Computerized tomography-guided biopsy disclosed synovial sarcoma. A general survey showed no evidence of distal metastasis. The patient received palliative debulking surgery, had a poor response to adjuvant radiotherapy and chemotherapy, and expired 6 months after operation. Due to the rarity of primary mediastinal synovial sarcoma, there is no standardized therapy. Broad surgical resection is the cornerstone of therapy. We report a patient with this rare disease and review the literature.

並列關鍵字

mediastinal tumor synovial sarcoma

延伸閱讀


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