外胚層發育不全兒童之牙科治療－病例報告

Dental Management of a Child with Ectodermal Dysplasia: Report of a Case

纪乃智(Nai-Chih Chi) ； 陳弘森(Hong-Sen Chen) ； 黃纯德(Shun-Te Huang) ； 蕭思郁(Szu-Yu Hsiao)

《臺灣兒童牙醫學雜誌》 6卷4期 (2006/12) Pp. 345-352

https://doi.org/10.6319/TJPD.2006.6(4).4

摘要

外胚層發育不全為一遺傳疾病，最常見的是性聯缺汗性類型。大部分發生在男性身上，會造成口腔內部份或是全部牙齒的缺失，並伴隨齒槽骨的不足或是沒有。患有外胚層發育不全的孩童其口腔復建因為牽涉到生長發育及階段性處置，因此常需要綜合牙科各專科的領域並有長遠的規劃。本病例為一12歲男孩，因為外胚層發育不全導致全口無牙。現階段我們以全口活動假牙改善他咀嚼與美觀的問題，長期規劃使用植體進行全口重建。定期追蹤評估患者之生長與家長配合程度，將有助於最終治療方式的選擇。

關鍵字

外胚層發育不全 ； 全口無牙 ； 治療計畫

並列摘要

Ectodermal dysplasia(ED)is an X-linked inherited disease. The most common is the hypohidrotic X-linked form affecting male subjects. ED with oligodontia or anodontia is characterized by deficiency or absence of alveolar ridges. Oral rehabilitation of children with ED should consider the growth and interim treatments at different stages. Multi-disciplinary collaboration and long-term treatment plan is needed. This 12-year-old boy diagnosed with ED presented a complete congenital absence of teeth. At his teen stage, a complete denture was fabricated to improve the mastication and appearance. Implant-supported prosthesis is planned in his adulthood. Regular check-ups and evaluation of child's growth and family's compliance will be helpful in the decision of final treatment.

並列關鍵字

Ectodermal Dysplasia ； Anodontia ； Treatment Plan