頸部之纖維瘤病－文獻回顧及病例報告

Desmoid Tumor of the Neck-Review of Literature and Report of a Case

蔡明魁(Ming-Kwai Tsai) ； 陳宏安(Hung-An Chen) ； 王東堯(Tung-Yiu Wang) ； 靳應台(Ying-Tai Jin)

《中華民國口腔顎面外科學會雜誌》 2卷2期 (1991/09) Pp. 54-60

https://doi.org/10.7104/CJOMS.199109.0054

摘要

Desmoid tumor是一種頗爲特殊的疾病，它在病理上雖是良性瘤，但在臨床上卻相當具有侵犯性和高度的再發率，甚至因而導致死亡。本文報告一位年僅8歲的病例，經外科切除後，追蹤9個月，迄今無再發跡象。desmoid tumor與外傷或Gardner's syndrome可能有關聯，而且經常併有鄰近骨質的異常。它的治療方式也有頗多爭議，而高度的再發率更提醒我們密切的術後追蹤是很重要的。

關鍵字

纖維瘤病 ； 軋耳德納氏症候群

並列摘要

Desmoid tumor is derived from musculoaponeurotic origin. Histo-logically it consists of interwining bundles of spindle cells in a collagen matrix, with normal mitosis and does not metastasize. Clinically, however, it is infiltrative and tends to recur locally. A case of demoid tumor in the neck of an eight-year-old boy was reported. He was presented with the chief complaint of a painless, firm swelling over the left mandibular angle regior for one month. The mass was found attach to the inferior border of the left mandibular angle. CT scan showed a well-defined homogenous mass with calcified spur near the mandibular angle. Microscopic findings from incisional biopsy were poor-defined tumor margin and bundles of spindle cells in a collagen matrix. The pathologic report was desmoid tumor. Under general anesthesia, the tumor was completely excised and the bone surface was trimmed and smoothened. After a follow-up period of nine months, no recurrence was noted.

並列關鍵字

desmoid tumor ； Gardner's syndrome